2-Hydroxy-2-methylbutaanzuur (standaard)

2-Hydroxy-2-methylbutanoic acid (Standard) is the analytical standard of 2-Hydroxy-2-methylbutanoic acid. This product is intended for research and analytical applications. 2-Hydroxy-2-methylbutanoic acid, an unusual metabolite, is associated with 2-hydroxyglutaric aciduria and maple syrup urine disease.

3739-30-8

12352211

Endogenous Metabolite; Reference Standards

Metabolic Enzyme/Protease; Others

Metabolic Disease

CCC(C)(O)C(O)=O

C5H10O3

118.13

[1]Dekant W, et al. Biotransformation of MTBE, ETBE, and TAME after inhalation or ingestion in rats and humans. Res Rep Health Eff Inst. 2001 May; (102) :29-71; discussion 95-109.

Room temperature

http://file.medchemexpress.com/batch_PDF/HY-W015874R/

Reference Standards