3-Hydroxyisovalerylcarnitine
Gecertificeerd

3-Hydroxyisovalerylcarnitine

Catalog #: TN7605-01
Maat: 10 mg

Kwaliteit

ISO Gecertificeerd

Levering

24-48 uur

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Gratis verzending vanaf €100
Technische Documentatie

Technische Specificaties

CAS Number

99159-87-2

Target

Endogenous Metabolite

Related Pathways

Metabolism

Bioactivity

3-Hydroxyisovalerylcarnitine is a carnitine derivative that may serve as a novel biomarker for biotin deficiency in humans, with its concentration increasing in such conditions. Biotin deficiency reduces the activity of biotin-dependent 3-methylcrotonyl-CoA carboxylase, hindering the conversion of 3-methylcrotonyl-CoA into 3-methylglutaconyl-CoA, and impairing the leucine catabolism pathway, resulting in elevated plasma 3-Hydroxyisovalerylcarnitine concentrations [1].

Smiles

O([C@@H](C[N+](C)(C)C)CC([O-])=O)C(CC(C)(C)O)=O

Molecular Formula

C12H23NO5

Molecular Weight

261.32

Shipping Conditions

Ice Packs

Storage Temperature

-20°C

Beschrijving

3-Hydroxyisovalerylcarnitine Beschikbaar in 10 mg. Bestel eenvoudig online met snelle levering.

Specificaties

Productnaam3-Hydroxyisovalerylcarnitine
Categorie
Beschikbare grootte10 mg
CatalogusnummerTN7605-01