BOLA3 Antilichaam

This gene encodes a protein that plays an essential role in the production of iron-sulfur (Fe-S) clusters for the normal maturation of lipoate-containing 2-oxoacid dehydrogenases, and for the assembly of the mitochondrial respiratory chain complexes. Mutation in this gene has been associated with multiple mitochondrial dysfunctions syndrome-2. Two alternatively spliced transcript variants encoding different isoforms with distinct subcellular localization have been reported for this gene (PMID:21944046) .

388962

Q53S33

Mouse, Rat

Recombinant fusion protein containing a sequence corresponding to amino acids 1-68 of human BOLA3 (NP_997717.2) .

Unconjugated

Primary Antibodies

Signal Transduction

Affinity purification

Mouse stomach

Batch dependent

PBS with 0.02% sodium azide, 50% glycerol, pH7.3.

None

Blue Ice

Store at -20˚ C. Avoid freeze / thaw cycles.

Observed: 12kDa

IgG

WB: 1:500 - 1:2000

BOLA3

Mouse heart

Mouse kidney

Rat liver

BolA family member 3

Homo sapiens

MMDS2, bolA-like protein 3, bolA homolog 3

WB

Liquid