CLN5 Antilichaam

This gene is one of eight which have been associated with neuronal ceroid lipofuscinoses (NCL) . Also referred to as Batten disease, NCL comprises a class of autosomal recessive, neurodegenerative disorders affecting children. The genes responsible likely encode proteins involved in the degradation of post-translationally modified proteins in lysosomes. The primary defect in NCL disorders is thought to be associated with lysosomal storage function.

1203

O75503

Human, Mouse, Rat

Recombinant fusion protein containing a sequence corresponding to amino acids 96-407 of human CLN5 (NP_006484.1) .

Unconjugated

Primary Antibodies

Neuroscience

Affinity purification

Mouse heart

Batch dependent

PBS with 0.02% sodium azide, 50% glycerol, pH7.3.

None

Blue Ice

Store at -20˚ C. Avoid freeze / thaw cycles.

Observed: 41kDa

IgG

CLN5

Rat heart

Ceroid-lipofuscinosis neuronal protein 5

Homo sapiens

Ceroid-lipofuscinosis neuronal protein 5, Protein CLN5, CLN5

WB, IHC

Liquid