Desmin (DES) Mouse Monoclonal Antibody [Kloon ID: LBI14E7]

This gene encodes a muscle-specific class III intermediate filament. Homopolymers of this protein form a stable intracytoplasmic filamentous network connecting myofibrils to each other and to the plasma membrane. Mutations in this gene are associated with desmin-related myopathy, a familial cardiac and skeletal myopathy (CSM), and with distal myopathies. [provided by RefSeq, Jul 2008]

Carrier-free (BSA/glycerol-free) Desmin mouse monoclonal antibody, clone LBI14E7

CDCD3; CSM1; CSM2; LGMD1D; LGMD1E; LGMD2R

Homo sapiens desmin (DES), transcript variant 1, mRNA.

1674

P17661

Unconjugated

Arrhythmogenic right ventricular cardiomyopathy (ARVC), Dilated cardiomyopathy, Hypertrophic cardiomyopathy (HCM)

Arrhythmogenic right ventricular cardiomyopathy (ARVC), Dilated cardiomyopathy, Hypertrophic cardiomyopathy (HCM)

IHC 1:1000

Lyophilized powder (original buffer 1X PBS, pH 7.3, 8% trehalose)

Lyophilized powder (original buffer 1X PBS, pH 7.3, 8% trehalose)

Druggable Genome

Stable for 1 year at -20°C from date of shipment. For maximum recovery of product, centrifuge the original vial after thawing and opening the cap. Aliquot will be stable at 4°C short term. For long-term storage, aliquot and store at -20°C or below. Stable for 12 months at -20°C. Avoid repeated freeze-thaw cycles.

DES

https://www.ncbi.nlm.nih.gov/gene/?term=1674

https://www.uniprot.org/uniprot/P17661