GAA Polyklonale Antilichaam, PE-Cy7 Vervoeging
Kwaliteit
ISO Gecertificeerd
Levering
24-48 uur
Technische Specificaties
This gene encodes acid alpha-glucosidase, which is essential for the degradation of glycogen to glucose in lysosomes. Different forms of acid alpha-glucosidase are obtained by proteolytic processing. Defects in this gene are the cause of glycogen storage disease II, also known as Pompe's disease, which is an autosomal recessive disorder with a broad clinical spectrum. Three transcript variants encoding the same protein have been found for this gene. [provided by RefSeq, Jul 2008].
70 kDa lysosomal alpha-glucosidase; Acid alpha glucosidase; Acid maltase; Aglucosidase alfa; Alpha glucosidase; GAA; Glucosidase alpha acid Pompe disease glycogen storage disease type II; Glucosidase alpha acid; Glucosidase alpha; LYAG; LYAG_HUMAN; Lysosomal alpha glucosidase.
2548
P10253
Cytoplasm, Cell membrane
• Rabbit
Human, Mouse
541-640/952
GAA
• Polyclonal
• IgG
PE-Cy7
KLH conjugated synthetic peptide derived from human GAA/Glucosidase alpha
WB
Purified by Protein A.
488nm/780nm
1µg/µl
WB (1:300-5000)
Aqueous buffered solution containing 0.01M TBS (pH7.4) with 1% BSA, 0.02% Proclin300 and 50% Glycerol.
Unmodified
Store at -20°C. Aliquot into multiple vials to avoid repeated freeze-thaw cycles.
2548
Rat, Dog, Sheep, Pig, Horse
Beschrijving
GAA Polyklonale Antilichaam, PE-Cy7 Vervoeging Beschikbaar in 100 µL. Bestel eenvoudig online met snelle levering.
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