IDUA Polyklonale Antilichaam

This gene encodes an enzyme that hydrolyzes the terminal alpha-L-iduronic acid residues of two glycosaminoglycans, dermatan sulfate and heparan sulfate. This hydrolysis is required for the lysosomal degradation of these glycosaminoglycans. Mutations in this gene that result in enzymatic deficiency lead to the autosomal recessive disease mucopolysaccharidosis type I (MPS I) . [provided by RefSeq, Jul 2008].

IDA; MPS1; Alpha-L-iduronidase; IDUA

3425

P35475

Cytoplasm

Human, Mouse

101-200/653

IDUA

Unconjugated

KLH conjugated synthetic peptide derived from human IDUA

WB, ELISA

Purified by Protein A.

1µg/µl

WB (1:300-5000), ELISA (1:500-1000)

0.01M TBS (pH7.4) with 1% BSA, 0.02% Proclin300 and 50% Glycerol.

Unmodified

Shipped at 4C. Store at -20C for one year. Avoid repeated freeze/thaw cycles.

3425