McCC2 Antibody - N-terminal regio : HRP (ARP46314 P050-HRP)

Methylcrotonoyl-CoA carboxylase 2 (beta)

MCCB, MCCCbeta

64087

Q9HCC0-2

Human, Mouse, Rat, Cow, Dog, Goat, Guinea Pig, Horse, Rabbit

The immunogen is a synthetic peptide directed towards the N-terminal region of Human MCCC2

This gene encodes the small subunit of 3-methylcrotonyl-CoA carboxylase. This enzyme functions as a heterodimer and catalyzes the carboxylation of 3-methylcrotonyl-CoA to form 3-methylglutaconyl-CoA. Mutations in this gene are associated with 3-Methylcrotonylglycinuria, an autosomal recessive disorder of leucine catabolism.

HUWE1; SUMO1; NEDD8; MDM2; PARK2; ADRB2; HDAC11; IFIT1; HSPD1; DYNC1H1; UBASH3B; INPPL1; EPS15; CUL3; UBC; EBNA-LP; ICT1; TERF2; TERF1

HRP: Horseradish Peroxidase

Polyclonal Antibody

WB

Affinity Purified

0.5 mg/ml

Cow: 100%; Dog: 93%; Goat: 86%; Guinea Pig: 100%; Horse: 79%; Human: 100%; Mouse: 100%; Rabbit: 93%; Rat: 100%

Liquid. Purified antibody is supplied in high phosphate PBS, 100 mm phosphate, 150 mM NaCl, pH 7.6.

All conjugated antibodies should be stored in light-protected vials or covered with a light protecting material (i.e. aluminum foil) . Conjugated antibodies are stable for at least 12 months at 4C. If longer storage is desired (24 months), conjugates may be diluted with up to 50% glycerol and stored at -20C to -80C. Freezing and thawing conjugated antibodies will compromise enzyme activity as well as antibody binding.

57kDa

Wet Ice

525

MCCC2

MCCC2

Rabbit

Methylcrotonoyl-CoA carboxylase beta chain, mitochondrial

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