MOGS Antilichaam

This gene encodes the first enzyme in the N-linked oligosaccharide processing pathway. The enzyme cleaves the distal alpha-1,2-linked glucose residue from the Glc (3) -Man (9) -GlcNAc (2) oligosaccharide precursor. This protein is located in the lumen of the endoplasmic reticulum. Defects in this gene are a cause of type IIb congenital disorder of glycosylation (CDGIIb) . Two transcript variants encoding different isoforms have been found for this gene.

7841

Q13724

Human, Mouse, Rat

Recombinant fusion protein containing a sequence corresponding to amino acids 60-320 of human MOGS (NP_006293.2) .

Unconjugated

Primary Antibodies

Other

Affinity purification

U-87MG

Batch dependent

PBS with 0.02% sodium azide, 50% glycerol, pH7.3.

None

Blue Ice

Store at -20˚ C. Avoid freeze / thaw cycles.

Observed: 80kDa

IgG

WB: 1:500 - 1:2000

MOGS

LO2

BxPC-3

OVCAR-3

Mouse Brain

Mouse Liver

Mannosyl-oligosaccharide glucosidase

Homo sapiens

GCS1, DER7, GCS1, CDG2B, CWH41

WB

Liquid