OPA1 Antilichaam - N-terminalgebied: FITC (ARP57715_P050-FITC)

Optic atrophy 1 (autosomal dominant)

NPG, NTG, MGM1, BERHS, largeG, MTDPS14

4976

E5KLK2

NP_570844

Human, Mouse, Rat, Cow, Dog, Guinea Pig, Horse, Rabbit, Zebrafish

This gene product is a nuclear-encoded mitochondrial protein with similarity to dynamin-related GTPases. It is a component of the mitochondrial network. Mutations in this gene have been associated with optic atrophy type 1, which is a dominantly inherited optic neuropathy resulting in progressive loss of visual acuity, leading in many cases to legal blindness. Multiple transcript variants encoding different isoforms have been found for this gene.

UBC; PARK2; MYC; HSP90AA5P; NIT2; HTRA2; NPTX1; NDUFS8; NDUFS1; NDUFA9; ILF3; HADHB; ECH1; DNASE2; APP; SMAD3; SMAD2; CAND1; CUL3; ELAVL1; MME

FITC: Fluorescein Isothiocyanate

Polyclonal Antibody

WB

Affinity Purified

0.5 mg/ml

Cow: 100%; Dog: 93%; Guinea Pig: 100%; Horse: 100%; Human: 100%; Mouse: 100%; Rabbit: 100%; Rat: 100%; Zebrafish: 79%

Liquid. Purified antibody supplied in 1x PBS buffer.

All conjugated antibodies should be stored in light-protected vials or covered with a light protecting material (i.e. aluminum foil) . Conjugated antibodies are stable for at least 12 months at 4C. If longer storage is desired (24 months), conjugates may be diluted with up to 50% glycerol and stored at -20C to -80C. Freezing and thawing conjugated antibodies will compromise enzyme activity as well as antibody binding.

102kDa

Wet Ice

924

OPA1

OPA1

Rabbit

Mitochondrial dynamin-like 120 kDa protein EMBL ADP90061.1

NM_130831

SPEETAFRATDRGSESDKHFRKVSDKEKIDQLQEELLHTQLKYQRILERL