PEX6 Antilichaam

This gene encodes a member of the AAA (ATPases associated with diverse cellular activities) family of ATPases. This member is a predominantly cytoplasmic protein, which plays a direct role in peroxisomal protein import and is required for PTS1 (peroxisomal targeting signal 1, a C-terminal tripeptide of the sequence ser-lys-leu) receptor activity. Mutations in this gene cause peroxisome biogenesis disorders of complementation group 4 and complementation group 6. Several transcript variants encoding different isoforms have been found for this gene.

5190

Q13608

Human, Mouse, Rat

Recombinant fusion protein containing a sequence corresponding to amino acids 741-980 of human PEX6 (NP_000278.3) .

Unconjugated

Primary Antibodies

Signal Transduction

Affinity purification

BT-474

Batch dependent

PBS with 0.02% sodium azide, 50% glycerol, pH7.3.

None

Blue Ice

Store at -20˚ C. Avoid freeze / thaw cycles.

Observed: 104kDa

IgG

WB: 1:500 - 1:2000

PEX6

K-562

Mouse liver

Mouse brain

Peroxisomal biogenesis factor 6

Homo sapiens

PEX6, peroxisomal biogenesis factor 6, PAF-2, PAF2, PXAAA1, peroxisomal AAA-type ATPase 1, peroxisome biogenesis factor 6

WB

Liquid