PPT1 Antilichaam - C-terminalgebied: FITC (ARP61425 P050-FITC)

Palmitoyl-protein thioesterase 1

PPT, CLN1, INCL

5538

P50897

NP_000301

Human, Mouse, Rat, Cow, Dog, Guinea Pig, Horse, Rabbit

The protein encoded by this gene is a small glycoprotein involved in the catabolism of lipid-modified proteins during lysosomal degradation. The encoded enzyme removes thioester-linked fatty acyl groups such as palmitate from cysteine residues. Defects in this gene are a cause of infantile neuronal ceroid lipofuscinosis 1 (CLN1, or INCL) and neuronal ceroid lipofuscinosis 4 (CLN4) . Two transcript variants encoding different isoforms have been found for this gene.

UBC; MDM2; GNAQ; TMEM9; NIT2; RIF1; NIPBL; SLC9A3R2; XRCC1; TCOF1; SGSH; FBXO6; MYC

FITC: Fluorescein Isothiocyanate

Polyclonal Antibody

WB

Affinity Purified

0.5 mg/ml

Cow: 86%; Dog: 100%; Guinea Pig: 85%; Horse: 93%; Human: 100%; Mouse: 77%; Rabbit: 92%; Rat: 83%

Liquid. Purified antibody supplied in 1x PBS buffer.

All conjugated antibodies should be stored in light-protected vials or covered with a light protecting material (i.e. aluminum foil) . Conjugated antibodies are stable for at least 12 months at 4C. If longer storage is desired (24 months), conjugates may be diluted with up to 50% glycerol and stored at -20C to -80C. Freezing and thawing conjugated antibodies will compromise enzyme activity as well as antibody binding.

34kDa

Wet Ice

306

PPT1

PPT1

Rabbit

Palmitoyl-protein thioesterase 1

NM_000310

GQAKETIPLQETSLYTQDRLGLKEMDNAGQLVFLATEGDHLQLSEEWFYA