PPT1 Mouse Monoclonal Antibody [Kloon ID: LBI1B10]

The protein encoded by this gene is a small glycoprotein involved in the catabolism of lipid-modified proteins during lysosomal degradation. The encoded enzyme removes thioester-linked fatty acyl groups such as palmitate from cysteine residues. Defects in this gene are a cause of infantile neuronal ceroid lipofuscinosis 1 (CLN1, or INCL) and neuronal ceroid lipofuscinosis 4 (CLN4) . Two transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq, Dec 2008]

Carrier-free (BSA/glycerol-free) PPT1 mouse monoclonal antibody, clone LBI1B10

CLN1; INCL; PPT

Homo sapiens palmitoyl-protein thioesterase 1 (PPT1), transcript variant 1, mRNA.

5538

P50897

Unconjugated

Fatty acid elongation in mitochondria, Lysosome, Metabolic pathways

Fatty acid elongation in mitochondria, Lysosome, Metabolic pathways

WB 1:2000

Lyophilized powder (original buffer 1X PBS, pH 7.3, 8% trehalose)

Lyophilized powder (original buffer 1X PBS, pH 7.3, 8% trehalose)

Druggable Genome

Stable for 1 year at -20°C from date of shipment. For maximum recovery of product, centrifuge the original vial after thawing and opening the cap. Aliquot will be stable at 4°C short term. For long-term storage, aliquot and store at -20°C or below. Stable for 12 months at -20°C. Avoid repeated freeze-thaw cycles.

PPT1

https://www.ncbi.nlm.nih.gov/gene/?term=5538

https://www.uniprot.org/uniprot/P50897