PQBP1 Antilichaam - middengebied: FITC (ARP32280 P050-FITC)

Polyglutamine binding protein 1

SHS, MRX2, MRX55, MRXS3, MRXS8, NPW38, RENS1

10084

O60828

NP_001027555

Human, Rat, Cow, Dog, Guinea Pig, Horse, Rabbit

The immunogen is a synthetic peptide directed towards the middle region of human PQBP1

This gene encodes a nuclear polyglutamine-binding protein that is involved with transcription activation. The encoded protein contains a WW domain. Mutations in this gene have been found in patients with Renpenning syndrome 1 and other syndromes with X-linked cognitive disability. Multiple alternatively spliced transcript variants that encode different protein isoforms have been described for this gene.

MAPRE1; GOLGA2; LZTS2; UBC; APBB1; WDR77; AQR; HNRNPH2; MRPL53; SLIRP; SRPRB; SUGP1; MRPS28; RPS6KA6; HRSP12; SCO2; ZC3H11A; UBL4A; VDAC3; RRBP1; RPS28; RBMS1; NDUFA7; IDH3G; APP; WBP11; RCVRN; LNX1; SF3A2; SFTPC; TXNL4A; TLX3; LRIF1; MED31; POLR2A; C14or

FITC: Fluorescein Isothiocyanate

Polyclonal Antibody

WB

Affinity Purified

0.5 mg/ml

Cow: 100%; Dog: 100%; Guinea Pig: 100%; Horse: 100%; Human: 100%; Rabbit: 93%; Rat: 100%

Liquid. Purified antibody supplied in 1x PBS buffer.

All conjugated antibodies should be stored in light-protected vials or covered with a light protecting material (i.e. aluminum foil) . Conjugated antibodies are stable for at least 12 months at 4C. If longer storage is desired (24 months), conjugates may be diluted with up to 50% glycerol and stored at -20C to -80C. Freezing and thawing conjugated antibodies will compromise enzyme activity as well as antibody binding.

30kDa

Lim, J., (2006) Cell 125 (4), 801-814

Wet Ice

265

PQBP1

PQBP1

Rabbit

Polyglutamine-binding protein 1

NM_001032383

LVSWLSPHDPNSVVTKSAKKLRSSNADAEEKLDRSHDKSDRGHDKSDRSH