SGSH Antilichaam - C-terminalgebied: HRP (ARP48124_P050-HRP)

N-sulfoglucosamine sulfohydrolase

HSS, SFMD, MPS3A

6448

P51688

NP_000190.1

Human, Mouse, Rat, Cow, Dog, Horse

The immunogen is a synthetic peptide directed towards the C-terminal region of human SGSH

This gene encodes one of several enzymes involved in the lysosomal degradation of heparan sulfate. Mutations in this gene are associated with Sanfilippo syndrome A, one type of the lysosomal storage disease mucopolysaccaridosis III, which results from impaired degradation of heparan sulfate. Transcripts of varying sizes have been reported but their biological validity has not been determined.

HRP: Horseradish Peroxidase

Polyclonal Antibody

WB

Affinity Purified

0.5 mg/ml

Cow: 79%; Dog: 86%; Horse: 93%; Human: 100%; Mouse: 79%; Rat: 79%

Liquid. Purified antibody is supplied in high phosphate PBS, 100 mm phosphate, 150 mM NaCl, pH 7.6.

All conjugated antibodies should be stored in light-protected vials or covered with a light protecting material (i.e. aluminum foil) . Conjugated antibodies are stable for at least 12 months at 4C. If longer storage is desired (24 months), conjugates may be diluted with up to 50% glycerol and stored at -20C to -80C. Freezing and thawing conjugated antibodies will compromise enzyme activity as well as antibody binding.

32kDa

Wet Ice

299

SGSH

SGSH

Rabbit

N-sulphoglucosamine sulphohydrolase

NM_000199.3

ARWELYDRSRDPHETQNLATDPRFAQLLEMLRDQLAKWQWETHDPWVCAP