SURF1 Antilichaam - N-terminaal gebied: Biotine (ARP61537 P050-Biotine)

Surfeit 1

SHY1, CMT4K, MC4DN1

6834

Q15526

NP_003163

Human, Cow, Guinea Pig, Horse

This gene encodes a protein localized to the inner mitochondrial membrane and thought to be involved in the biogenesis of the cytochrome c oxidase complex. The protein is a member of the SURF1 family, which includes the related yeast protein SHY1 and rickettsial protein RP733. The gene is located in the surfeit gene cluster, a group of very tightly linked genes that do not share sequence similarity, where it shares a bidirectional promoter with SURF2 on the opposite strand. Defects in this gene are a cause of Leigh syndrome, a severe neurological disorder that is commonly associated with systemic cytochrome c oxidase deficiency.

UBC; PTGES3; CHCHD4; SFXN3; NDUFA12; NDUFAF3; SAMM50; FKBP8; UQCRC1; SRSF5; ABCD3; NDUFV2; NDUFS8; NDUFS3; NDUFB8; ABCC1; CYC1; COX15

Biotin

Polyclonal Antibody

WB

Affinity Purified

0.5 mg/ml

Cow: 79%; Guinea Pig: 86%; Horse: 86%; Human: 100%

Liquid. Purified antibody supplied in 1x PBS buffer.

All conjugated antibodies should be stored in light-protected vials or covered with a light protecting material (i.e. aluminum foil) . Conjugated antibodies are stable for at least 12 months at 4C. If longer storage is desired (24 months), conjugates may be diluted with up to 50% glycerol and stored at -20C to -80C. Freezing and thawing conjugated antibodies will compromise enzyme activity as well as antibody binding.

33kDa

Wet Ice

300

SURF1

SURF1

Rabbit

Surfeit locus protein 1

NM_003172

GLRAAGLGRAPASAAWRSVLRVSPRPGVAWRPSRCGSSAAEASATKAEDD