HMGCL Antilichaam - N-terminaal gebied: Biotine (ARP41686_T100-Biotine)

3-hydroxymethyl-3-methylglutaryl-CoA lyase

HL

3155

P35914

NP_000182

Human, Mouse, Rat, Cow, Dog, Guinea Pig, Horse, Rabbit, Zebrafish

The immunogen is a synthetic peptide directed towards the N terminal region of human HMGCL

The deficiency of HMGCL is related to an autosomal recessive branched chain organic aciduria.

GTF2B; PEX5; ADAMTS10; RNF126; ARL6IP1; DNAJA1; HES1; MS4A7

Biotin

Polyclonal Antibody

WB

0.5 mg/ml

Cow: 93%; Dog: 100%; Guinea Pig: 100%; Horse: 100%; Human: 100%; Mouse: 100%; Rabbit: 92%; Rat: 100%; Zebrafish: 91%

Liquid. Purified antibody supplied in 1x PBS buffer.

All conjugated antibodies should be stored in light-protected vials or covered with a light protecting material (i.e. aluminum foil) . Conjugated antibodies are stable for at least 12 months at 4C. If longer storage is desired (24 months), conjugates may be diluted with up to 50% glycerol and stored at -20C to -80C. Freezing and thawing conjugated antibodies will compromise enzyme activity as well as antibody binding.

36kDa

Fu, Z., (2006) J. Biol. Chem. 281 (11), 7526-7532

Wet Ice

325

HMGCL

HMGCL

Rabbit

Hydroxymethylglutaryl-CoA lyase, mitochondrial

NM_000191

WVPQMGDHTEVLKGIQKFPGINYPVLTPNLKGFEAAVAAGAKEVVIFGAA