NAGLU Antibody - N-terminal regio : HRP (ARP58644_P050-HRP)

N-acetylglucosaminidase, alpha

NAG, CMT2V, MPS3B, UFHSD, MPS-IIIB

4669

P54802

NP_000254

Human, Cow, Dog, Pig

The immunogen is a synthetic peptide directed towards the N-terminal region of Human NAGLU

This gene encodes an enzyme that degrades heparan sulfate by hydrolysis of terminal N-acetyl-D-glucosamine residues in N-acetyl-alpha-D-glucosaminides. Defects in this gene are the cause of mucopolysaccharidosis type IIIB (MPS-IIIB), also known as Sanfilippo syndrome B. This disease is characterized by the lysosomal accumulation and urinary excretion of heparan sulfate.

UBC; FBXO6

HRP: Horseradish Peroxidase

Polyclonal Antibody

WB

Affinity purified

0.5 mg/ml

Cow: 83%; Dog: 92%; Human: 100%; Pig: 79%

Liquid. Purified antibody is supplied in high phosphate PBS, 100 mm phosphate, 150 mM NaCl, pH 7.6.

All conjugated antibodies should be stored in light-protected vials or covered with a light protecting material (i.e. aluminum foil) . Conjugated antibodies are stable for at least 12 months at 4C. If longer storage is desired (24 months), conjugates may be diluted with up to 50% glycerol and stored at -20C to -80C. Freezing and thawing conjugated antibodies will compromise enzyme activity as well as antibody binding.

81kDa

Wet Ice

743

NAGLU

NAGLU

Rabbit

Alpha-N-acetylglucosaminidase

GVLLLAGAGGAAGDEAREAAAVRALVARLLGPGPAADFSVSVERALAAKP